Dyke-Davidoff-Masson syndrome: a combination of clinical and radiological signs not to be missed.

A 21-year-old man presented with complex partial status epilepticus. His past medical history was marked by epilepsy and his examination disclosed atrophy of the right limbs and hemiparesis in the same side of the body. A brain CT scan showed atrophy of the entire left hemisphere, with prominent sulci, enlargement of the lateral ventricle and overdevelopment of the frontal sinuses on the left side (see figure). Dyke-Davidoff -Masson syndrome is an uncommon con genital or childhood-onset acquired neurologic syndro me, presenting mainly with complete hemiparesis, recurrent seizures and non-progressive chronic encephalopathy1,2. Neuroimaging features are characterized by unilateral cerebral atrophy with ipsilateral hypertrophy of pa ranasal sinuses2.